Article

We report a case of inflammatory cerebral amyloid angiopathy (CAA) that led to
rapid cognitive decline, seizures, visual hallucinations, hyperproteinorrachia
and right hemispheric leukopathy. Brain biopsy gave the diagnosis of CAA.
Although no inflammatory infiltrate was found in the biopsy sample,
corticosteroids led to a regression of the radiological lesions without
significant clinical improvement. CAA is a rare disease,
defined by lesions of
classical cerebral amyloid angiopathy and perivascular infiltrates in contact
with the affected vessels. In cases of rapidly progressive dementia associated
with leukopathy, inflammatory amyloid angiopathy should be considered as
cognitive disorders may improve after immunosuppressive therapy.
CI - Copyright (c) 2015 Elsevier Masson SAS. All rights reserved.

Langue : FRANCAIS